Ebsteins Disease: About Two Cases Discovered Following a Rhythm Disorder
Author(s):
Z. BENNOUI, M. ABDELBAKI
Ebstein's disease is a rare congenital heart disease. It is characterized by the low insertion of one or two tricuspid leaflets leading to atrialization of the right ventricle. The clinical forms vary, ranging from neonatal anasarca to right heart failure and arrhythmia in adolescents and adults. It can remain asymptomatic for a long time, and the discovery is fortuitous following a preoperative assessment for extracardiac surgery or other reasons. We report two clinical cases of Ebstein's disease, different in their circumstances of discovery: in the first case, the disease was discovered following an assessment of right bundle branch block with late left extrasystoles in a 20-year-old patient, and the second case, during an assessment of palpitations in a 13-year-old patient. Through these cases, we will review the circumstances of discovery of the disease by recalling the different types of cardiographic echo and therapeutic management.