Primary Pulmonary Ewing Sarcoma or Askin Tumor (PNET of the Thoracopulmonary Region) - A Rare Clinical Case in our Practice
Author(s):
Lena Marinova, Vaska Vasileva, Nikolay Kahchiev, Nadejda Tsvetkova and Bistra Yordanova
Primary pulmonary Ewing sarcoma is a rare disease belonging to the �?wing sarcoma tumor family. The origin of these rarely diagnosed primary undifferentiated neoplasms with possible localization in different organs and tissue structures is still unknown. We present a rare clinical case of primary pulmonary extraskeletal Ewing sarcoma in a woman 35 years old. The purpose of this article is to emphasize the difficult histological and differential diagnosis, requiring a wide panel of immunohistochemical markers. Despite the maximum possible radical surgery, given the local biological malignancy of this exceptionally rare tumor with a poor prognosis, we performed postoperative intensity modulated radiotherapy (IMRT).